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Vol.2 , No. 5, Publication Date: Oct. 29, 2015, Page: 61-64
 and Early Repolarization Syndrome (ERS). We presented herein a 46_year_old women with no familial history of sudden death. She was hospitalized for ventricular tachycardia with a lipothymia episode. We recorded in the electrophysiology study a fractionated electrogram in the same time with ventricular depolarization after fascicular electrograms. This fractionated electrograms precede slurring of the terminal portion of the R wave (J wave) and the atrial stimulation with extrastimulus decaled the fractionated electrograms responsible of Brugada Syndrome type 1 on the ECG. Brugada Syndrome (BrS) and Early Repolarization Syndrome (ERS) suggesting that two syndromes with J wave’s disorders have the same mechanism: wave front fragmentation in the anterolateral free wall of the RVOT responsible of ventricular tachycardia (VT).&picture=http://www.aascit.org/aascit/decorators/img/journal/906.jpg)
| [1] | S. Marrakchi, Cardiology Department Abderhamen Mami Hospital Ariana, Medical School of Tunis, University Manar II, Tunis, Tunisia. |
| [2] | I. Kammoun, Cardiology Department Abderhamen Mami Hospital Ariana, Medical School of Tunis, University Manar II, Tunis, Tunisia. |
| [3] | S. Kachboura, Cardiology Department Abderhamen Mami Hospital Ariana, Medical School of Tunis, University Manar II, Tunis, Tunisia. |
Recent studies have suggested an association between several channulopathy diseases. However, the mechanism remains unclear. The aim of this case was to demonstrate the relation between Brugada Syndrome (BrS) and Early Repolarization Syndrome (ERS). We presented herein a 46_year_old women with no familial history of sudden death. She was hospitalized for ventricular tachycardia with a lipothymia episode. We recorded in the electrophysiology study a fractionated electrogram in the same time with ventricular depolarization after fascicular electrograms. This fractionated electrograms precede slurring of the terminal portion of the R wave (J wave) and the atrial stimulation with extrastimulus decaled the fractionated electrograms responsible of Brugada Syndrome type 1 on the ECG. Brugada Syndrome (BrS) and Early Repolarization Syndrome (ERS) suggesting that two syndromes with J wave’s disorders have the same mechanism: wave front fragmentation in the anterolateral free wall of the RVOT responsible of ventricular tachycardia (VT).
Keywords
Early Repolarization Syndrome, Brugada Syndrome, Ventricular Tachycardia
Reference
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