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Vol.2 , No. 4, Publication Date: Jul. 22, 2015, Page: 30-34
| [1] | Gobinda Kanti Paul, Department of Cardiology, Mymensingh Medical College (MMC), Mymensingh, Bangladesh. |
| [2] | M. Saiful Bari, Department of Cardiology, Mymensingh Medical College (MMC), Mymensingh, Bangladesh. |
Ebstein anomaly is a congenital abnormality of the tricuspid valve in which there is apical displacement typically of the septal leaflet as well as tethering of the lateral leaflet to the ventricular wall. This results in coaptation of the tricuspid leaflets in a position displaced toward the right ventricular apex and creates an atrialized portion of the right ventricle. The degree of displacement can be highly variable and can range from as little as 12 mm to several centimeters. A variety of cardiac abnormalities are associated with Ebstein’s anomaly, including atrial septal defect, conduction system abnormalities, patent foramen ovale, pulmonary stenosis or atresia and ventricular septal defect. Ebstein’s anomaly is mild in most adults who have it, so they do not need surgery. But sometimes the tricuspid valve leaks severely enough to result in heart failure or cyanosis. Then surgery may be required. When patients of all ages are taken together, the predicted mortality is approximately 50% by the fourth or fifth decade. We present here an uncommon presentation of this complex congenital heart defect in a 75 years old man.
Keywords
Ebstein’s Anomaly, Congenital Heart Defect, Tricuspid Regurgitation
Reference
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